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Pelizaeus-Merzbacher 병 환자의 외래전신마취 하 치과치료 -증례보고- : Dental Treatment of a Patient with Pelizaeus-Merzbacher Disease under Outpatient General Anesthesia -A Case Report-

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Authors

김태경; 신차욱; 김현정; 염광원; 서광석

Issue Date
2007
Publisher
대한치과마취과학회
Citation
대한치과마취과학회지 2007; 7: 18-21.
Keywords
Dental procedureGeneral anesthesiaLeukodystrophyPelizaeus-Merzbacher disease
Abstract
Pelizaeus-Merzbacher disease (PMD) can be defined as an X-linked recessive leukodystrophy that is caused by a mutation in the proteolipid protein gene on chromosome Xq22. PMD is one of a group of progressive, degenerative disorders of the cerebral white matter known as the leukodystrophies. Due to the progressive nature of the disorders and their devastating effects on the central nervous system, these children frequently require anesthesia during imaging procedures such as MRI or during various surgical procedures. Anesthetic concerns in theses cases include high prevalence of seizure disorders, gastroesophageal reflux with the risk of aspiration, airway complications related to poor pharyngeal muscle control and copious oral secretions, and mental retardation. We report a successful anesthetic management in a patient with PMD for dental procedures.
ISSN
1598-4044
Language
Korean
URI
http://uci.or.kr/G100:I100-KOI(KISTI1.1003/JNL.JAKO200734514833065)

https://hdl.handle.net/10371/47993
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