Congenital Cystic Disease of the Kidney(SNUCH CPC-38)

Abstract

(Clinicopathologic Conference) This male newborn was admitted to SOHWA Children's Hospital on Aug 27, 1987 because of abdominal distension and anuria. He was born by Cesarian section due to breech presentation on July 28, 1987 at KURO Hospital The gestational age was 37 +4 weeks and the membrane ruptured 2 hours before the delivery. At birth, his body weight was 2.370gm. He had been admitted to KURO Hospital under the impression of hydronephrosis and acute renal failure until Aug. 18, 1987 (22nd day of Iife). At birth he had good Apgar scores. But weight gain was poor, and on the 15th hospital day an abdominal mass in the left upper quadrant was palpated. The abdominal sonography showed bilateral hy-dronephrosis. Serum BUN and creatinine were 188 mg% and 5,3 mg%. Serum Na was 132mEq/L, K 6.5 mEq/L, CI 97 mEq/L and CO26 mEq/L. Peritoneal dialysis was done with peritosol from the 15th to 16th hospital day. On the 20th hospital day, serum BUN and creatinine became 118 mg% and 3.4 mg%.Blood electrolytes showed serum Na 116mEq/L,K 6.5 mEq/L, CI 89 mEq/L and CO2 17.5 mEq/L.IVP revealed non-visualization of both kidneys. At the 22nd hospital day, he was discharged against advice.