Extralobar Pulmonary Sequestration associated with Congenital Diaphragmatic Hernia

Abstract

Authors reported a case of extralobar pulmonary sequestration at the site of congenital diaphragmatic hernia in a 2 day old infant. The accessory lung was found incidentally during a reparative surgery for a left Bochdalek hernia. This mass, 2cm in size, was far apart from the poorly aerated left lung, and was embedded within the membraneous tissue of the diaphragmatic hernial sac. Neither bronchial nor pulmonary arterial conncction was seen. The hernia was successfully repaired and the accessory lung mass was removed. Microscopically the removed mass consisted entirely of terminal bronchiolar structures with focal cystic dila ta tion and abun dan t stroma which contained scattered striated muscle fibers. No evidence of alveolar differentiation was recognized.