Potter 증후근(1부검 증례보고)
Potter's Syndrome (An Antopsy Case Report in a DeadbornFetus)

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지제근; 박태동
Issue Date
서울대학교 의과대학
Seoul J Med 1979;20(2):146-152
In 1946 Potter described a series of 20 cases in
infants in whom bilateral absence of the kidneys was
associated with hypoplasia of the lungs and a chao
racteristic face. This combination has been known as
Potter's syndrome after the first describer, E.L. Potter.
The main facial features she described were an incr·
eased space between the eyes, a promnient fold which
arises at the inner canthus and sweeps downward and
laterally below the eyes, unusual flattening of the
nose. excessive recession of the chin. moderate enlargement
and decreased chondrification of the ears, and
a suggestion of premature senility. The mother of this patient, 28 year old, para 0-01-
0, was admitted to a local clinic with the chief
complaint of amenorrhea for 35 weeks in labor and
diagnosed as fetal death in utero.There was no known exposure to infection or drug during this pregnancy.
She delivered a male baby rather macerated, with
cord coiling around the neck twice. Autopsy findings
were; crown-rump. 27cm: crown-heel, 42cm; body
weight, 2.2kg. The abnormal facial features were
low-set and floppy ears, receding chin with dimpling
between lower lip and chin, flattened nose, less
prominent fold and the appearance of premature
senility, The lungs showed hypoplasia with pale color
and incomplete lobation, weighing 5.9gm and 6.5gm
in the left and the right side, respectively. Microscopically,
the alveoli were crowded and revealed
tubular structure without specific abnormality except
for a general reduction of the parenchymal bulk.
There was a bilateral absence of kidneys. and retroperitoneal
space was replaced by slightly enlarged and
disc-shaped adrenal glands. Both ureters were absent
together with hoth renal arteries. The urinary bladder
was elongated superoinferiorly to show a tubular structure. and its wall was attenuated in thickness.
The left testis was located in the abdomen but
the right testis was located in scrotun, embedded in
hematoma. There was an extradigit of the right hand.
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College of Medicine/School of Medicine (의과대학/대학원)Dept. of Medicine (의학과)The Seoul Journal of MedicineThe Seoul Journal of Medicine Vol. 20 No.2 (1979)
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