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Combined focal myoclonus and dystonia secondary to a cerebellar hemorrhage: a case report

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Authors
Shen, Guangxun; Nan, Guangxian; Shin, Chae-Won; Park, Hyeyoung; Lee, Kwee-Yum; Jeon, Beomseok
Issue Date
2016-11-17
Publisher
BioMed Central
Citation
BMC Neurology, 16(1):228
Keywords
MyoclonusDystoniaCerebellar lesionMagnetic resonance imagingElectromyography
Description
This article is distributed under the terms of the Creative Commons Attribution 4.0
International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and
reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to
the Creative Commons license, and indicate if changes were made.
Abstract
Abstract

Background
Myoclonus is a clinical sign characterized by sudden, brief jerky, shock-like involuntary movements of a muscle or group of muscles. Dystonia is defined as a syndrome of sustained muscle contractions, frequently causing twisting and repetitive movements or abnormal postures. Cases of myoclonus or dystonia secondary to a structural lesion in the cerebellum have been reported. However, there has never been a reported case of combined myoclonus and dystonia secondary to a cerebellar lesion.


Case presentation
Herein, we report a 22-year-old female patient with sudden-onset myoclonic jerks, dystonic posture and mild ataxia in the right upper extremity. At age 19, she experienced sudden headache with vomiting. The neurological examination showed ataxia, myoclonus and dystonia in the right upper extremity. Brain images demonstrated a hemorrhage in the right cerebellar hemisphere secondary to a cavernous malformation. After resection of the hemorrhagic mass, headache with vomiting disappeared and ataxia improved, but myoclonus and dystonia persisted.


Conclusions
It is the first report of combined focal myoclonus and dystonia secondary to a cerebellar lesion.
Language
English
URI
http://hdl.handle.net/10371/100554
DOI
https://doi.org/10.1186/s12883-016-0745-6
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College of Medicine/School of Medicine (의과대학/대학원)Dept. of Neurology (신경과학교실)Journal Papers (저널논문_신경과학교실)
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