이중 여성 외부 생식기 (1부검 증례)

Abstract

Double external genitalia is a rare anomaly in both sexes. In boys it has been reported by many authors since it was first reported by Ballantyne in 1895, as the rarest malformation of the penis, and some cases were associated with imrerforate anus CCcchrane et a!' , in 1942). But in girls. tbere is no case of double external genitalia in English literatures available We report an autopy case of a girl who had double external genitalia and lower two thirds of vagina associated with low type of imperforate anus and several fistula tracts. This girl was a full term infant of a 40 year old mother and died on the 7th day of life due to sepis. She had double anal pits without vcr foration and double vestibules surrounded by indepen 111 dent double labia minora and labia majora_ In the right vestibule there were both urethral orifice and vaginal introitus which extended to urinary bladder and uterus in normal fashion. Just above the introitus , the right vagina revealed rectovaginal fistula from which meconium was passed The left vestibule had only vaginal introitus which ended blindly at the lower two thirds of full length, and instead, is connected with the vagina of opposite side and urinary bladde r. In other words intervaginal and vaginovesical fistula were presen t. Beside these complex anomalies, there were Meckel s diverticulum at IDcm proximal to ileocecal junction patent ductus arteri osus and atrial septal defect of ostium II type