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Unilateral (probable) moyamoya disease: long-term follow-up of seven cases

Cited 24 time in Web of Science Cited 22 time in Scopus
Authors
Seol, Ho Jun; Wang, Kyu-Chang; Kim, Seung-Ki; Lee, Chang Sub; Lee, Dong Soo; Kim, In-One; Cho, Byung-Kyu
Issue Date
2005-10-13
Publisher
Springer-Verlag
Citation
Childs Nerv Syst. 2006 Feb;22(2):145-50. Epub 2005 Oct 12.
Keywords
Cerebral AngiographyCerebrovascular Disorders/*etiology/pathology/radiographyChildChild, PreschoolDisease ProgressionFemale*Functional LateralityHumansInfantLongitudinal StudiesMaleMoyamoya Disease/*complications/*pathology/radiographyRetrospective StudiesReview Literature as TopicTomography, Emission-Computed, Single-Photon/methods
Abstract
OBJECTS: Some cases of unilateral involvement have angiographic findings on the affected side which resemble those of definite cases of moyamoya disease (MMD). We analyzed these cases to determine whether the entity "unilateral MMD" actually exists and whether unilateral involvement represents only the early phase of the pathologic process found in definitive bilateral disease. METHODS: Between 1988 and 2000, seven cases of unilateral MMD were evaluated. The male-to-female ratio was 2:5, mean age was 5.1 years (7 months to 8 years), and mean follow-up duration was 64.7 months. The presenting symptoms of these cases were similar to those of definite MMD, and no familial occurrence was found. Two of the seven unilateral MMD cases showed progression to bilateral involvement. However, the remaining cases showed no evidence of contralateral progression during the follow-up period. CONCLUSIONS: Most cases of unilateral MMD seem to be an unusual form of stenoocclusive process of the proximal intracranial arteries, distinguishing the condition from definite MMD. Surgical treatment on the symptomatic side and close observation for signs of bilateral involvement are necessary.
ISSN
0256-7040 (Print)
Language
English
URI
http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&dopt=Citation&list_uids=16220301

http://hdl.handle.net/10371/15267
DOI
https://doi.org/10.1007/s00381-005-1234-1
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College of Medicine/School of Medicine (의과대학/대학원)Neurosurgery (신경외과학전공)Journal Papers (저널논문_신경외과학전공)
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