S-Space College of Medicine/School of Medicine (의과대학/대학원) Pathology (병리학전공) Journal Papers (저널논문_병리학전공)
Degos' disease (malignant atrophic papulosis) as a fatal cause of acute abdomen: report of a case
Cited 12 time in Web of Science Cited 10 time in Scopus
- Issue Date
- Springer Verlag
- Surg Today (2008) 38:866–870
- Degos’ disease ; Malignant atrophic papulosis ; Small bowel
- Degos' disease, otherwise known as "malignant atrophic papulosis," is a rare condition characterized by typical cutaneous lesions. Its involvement of the gastrointestinal (GI) tract is usually associated with a poor prognosis. We report a case of Degos' disease with GI involvement, which ultimately caused peritonitis, sepsis, and death, despite all treatment measures. A 59-year old woman was admitted to our hospital with acute generalized abdominal pain. The patient had presented initially with multiple skin lesions 2 years earlier, and even with surgery for small-bowel perforation 10 months before this admission, Degos' disease had not been diagnosed. Explorative laparotomy revealed multifocal, ischemic changes in the small bowel with perforation in the mid-jejunum. After the operation, she suffered recurrent small-bowel fistulas and died within 3 months. In a patient with acute abdominal pain and typical atrophic papules, clinicians should retain a high index of suspicion for Degos' disease with GI involvement, even though it is rare.
- 0941-1291 (print)
- Files in This Item: There are no files associated with this item.
- Appears in Collections:
- College of Medicine/School of Medicine (의과대학/대학원)Pathology (병리학전공)Journal Papers (저널논문_병리학전공)
Items in S-Space are protected by copyright, with all rights reserved, unless otherwise indicated.