Juvenile Angiodysplasia of Gut

Abstract

Angiodysplasia or arteriovenous malformation of the gastrointestinal tract in younger patients is different from "classic" angiodysplasia in older patients, by age of onset, clinical presentation, location of the lesion and diverse histologic features, We report two cases of juvenile angiodysplasia of the gut. The diagnosis was suspected by radionuclide blood pool scan and was confirmed by resection and pathological examination, Both cases were girls of 5 years and 12 years of age, and the lesions were in the jejunum and ileum, Grossly, one case showed multiple petechiae and another case showed a hemorrhagic polypoid mass, Microscopically, the lesions were composed of irregularly dilated vascular channels in mucosa and submucosa with abnormal proliferation of arteries and veins in submucosa, Both cases are free of recurrence after local resection,