Darier`s disease: variable clinical presentation and a fatal outcome

Abstract

A 34-year-old man was admitted with worsening skin lesions with persistent fever and chills. The skin lesions had first appeared on the neck as multiple erythematous papules at the age of 5 years. They extended to the face, trunk and groin, and he was diagnosed with Darier s disease (DD) at 15 years of age. He denied any family history of skin problems and his two daughters, aged 4 and 2 years, had not shown any evidence of DD at that point.