Detailed Information

Fallot씨 사징, 반상심내막 섬유증과 신위축증 및 고혈압을 수반한 안전내장 전위증 : Situs Inversus Viscerum Totalis, Accompanied by Tetralogy of Fallot, Localized Endocardial Fibrosis, and Nephrosclerosis with Hypertension

DC Field Value Language
dc.identifier.citationSeoul J Med, Vol.2 No.3, pp. 165-174-
dc.description.abstractto have situs inversus totalis including dextrocardia.
and tetralogy of Fallot.
A surgical palliation was tried, but it was found to
be of little avail. Post-mortem examination revealed
the following:
All thoraco-abdominal viscera and vessels were in
the mirror-image position of the normal.
The heart was in the right hemithorax in the mirror
-irnage position of the normal, the cardiac axis directing
right-lateralwards. The heart was globular in
shape, enormously large, and weighed 500 gms. On
section, the heart revealed tetralogy of Fallot in
dextrocardiac position, including marked pulmonary
stenosis of infundibular type with hypoplasia of pulmonary
artery, marked hypertrophy of left-sided right
ventricle (venous ventricle), large interventricular
septal defect at the pars membranacea, and sinistroposition
and over-riding of the aorta.
There was a large 6X3cm. localized elongatedrhomboid
area of endocardial thickening in the rightsided
left ventricle(arterial ventricle), that revealed
microscopically markedly increased noninflamed loose
fibrous connective tissue with some elastic fibers extending
into the adjacent and underlying myocardium.
Multiple small fenestration of the aortic valve leaflets
and marked dil-atation of bilateral bronchial arteries
in the mirror image position were observed.
An aberrant parathyroid gland was observed over
the trachea, 1.5 em. distal to the right lower pole of
the thyroid gland.
The right and left kidneys weighed 120 gms, and 100
gms, respectively, and showed bilateral diffuse but
mild arteriolar nephrosclerosis. Clinically this patient
had mild hypertension. The aorta and its main branches
showed marked atherosclerosis.
There were moderate generalized passive congestion
of all viscera and clubbed fingers and toes.
A small confluent nodular lesion of fibrocaseous
tuberculosis that was partly calcified was observed in
the right upper lobe of the lungs.
This is believed to be the first autopsy case of
congenital anomaly of the heart of this type reported
in the Korean literature.
dc.publisher서울대학교 의과대학-
dc.titleFallot씨 사징, 반상심내막 섬유증과 신위축증 및 고혈압을 수반한 안전내장 전위증-
dc.title.alternativeSitus Inversus Viscerum Totalis, Accompanied by Tetralogy of Fallot, Localized Endocardial Fibrosis, and Nephrosclerosis with Hypertension-
dc.typeSNU Journal-
dc.contributor.AlternativeAuthorLee, Sung Soo-
dc.contributor.AlternativeAuthorLee, Dae il-
dc.contributor.AlternativeAuthorKim, Yong Il-
dc.contributor.AlternativeAuthorLee, Young Kyun-
dc.citation.journaltitle서울 의대 잡지-
dc.citation.journaltitle서울 의대 학술지-
dc.citation.journaltitleSeoul Journal of Medicine-
Appears in Collections:
Files in This Item:


Item View & Download Count

  • mendeley

Items in S-Space are protected by copyright, with all rights reserved, unless otherwise indicated.